Polysplenia Syndrome, Heterotaxy with Jejunal Atresia: A Case Report

Authors

  • Mazen O. Kurdi King Abdulaziz University
  • Abdel-Rahman R. Abdel-Halim King Abdulaziz University

DOI:

https://doi.org/10.4197/Med.20-3.9

Keywords:

Polysplenia syndrome; Heterotaxy; Dextrogastria; Situs ambiguous; Jejunal atresia; Intestinal atresia; Asplenia

Abstract

Heterotaxy is defined as an abnormality where the internal thoracoabdominal organs show abnormal arrangements across the left-right axis of the body. It might affect the stomach alone, i.e. dextrogastria. This anomaly can be combination of dextrogastria with functional asplenia (asplenic or hyposplenic) and other visceral heterotaxy with possible malrotation. Heterotaxy is rare condition and its association with intestinal atresia is almost very rarely reported in the literature. Presented is a case of heterotaxy with dextrogastria, multiple small splenules and associated with Type 2 jejunal atresia with brief review of the literature.  

Author Biographies

Mazen O. Kurdi, King Abdulaziz University

Department of Surgery, Divison of Pediatric Surgery

Abdel-Rahman R. Abdel-Halim, King Abdulaziz University

Department of Surgery, Division of Pediatric Surgery

Published

2013-07-01

How to Cite

Kurdi, M. O., & Abdel-Halim, A.-R. R. (2013). Polysplenia Syndrome, Heterotaxy with Jejunal Atresia: A Case Report. Journal of King Abdulaziz University - Medical Sciences, 20(3), 101-109. https://doi.org/10.4197/Med.20-3.9

Issue

Section

Case Reports

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